What is the rate of hearing loss associated with Pierre Robin syndrome?

Pierre Robin syndrome (PRS) is a condition characterized by a triad of features: micrognathia (small jaw), glossoptosis (downward displacement of the tongue), and cleft palate. The hearing loss associated with this syndrome has been studied extensively, and it's found that a significant portion of individuals with PRS can experience hearing impairment due to the anatomical and functional complications related to the condition.

The reported rate of hearing loss in children with Pierre Robin syndrome has been documented to be around 60%. This rate takes into account factors such as the impact of the cleft palate on the middle ear's ventilation, which can lead to otitis media with effusion (OME), a common cause of conductive hearing loss. Additionally, the anatomical features associated with micrognathia and glossoptosis can cause various audiological problems.

Understanding this statistic is crucial for healthcare professionals involved in the care of patients with PRS, as it highlights the importance of regular auditory screening and the need for early intervention and management strategies to address hearing loss and its potential impact on speech and language development.